年发病率为1~2/10万,男女比例为2:3。[1]Tos M, Charabi S, Thomsen J. Clinical experience with vestibular schwannomas: epidemiology, symptomatology, diagnosis, and surgical results. Eur Arch Otorhinolaryngol. 1998;255:1-6.http://www.ncbi.nlm.nih.gov/pubmed/9592666?tool=bestpractice.com[2]Jones KD. Summary: vestibular schwannoma (acoustic neuroma) consensus development conference. Neurosurgery. 1993;32:878-879.http://www.ncbi.nlm.nih.gov/pubmed/8492871?tool=bestpractice.com 因MRI的普及,更多小肿瘤被检测到。听神经瘤占所有颅内肿瘤的6%,占小脑桥脑角肿瘤的70%至80%。所有种族和族裔发病率大致相等。