所有关于肠旋转异常的流行病学数据都倾向于远远低估了实际的发病率,因为有许多不完全旋转的患者无临床症状而从未诊断。在上消化道造影检查中偶然发现的肠旋转异常疾病占0.2%。[1]Kantor JL. Anomalies of the colon: their roentgen diagnosis and clinical significance: Resume of 10 years study. Radiology. 1934;23:651-662.这个分母也具有一定的误导性,因为这些病通常有某些疾病而做这个检查。尸检报告肠旋转不良的发生率为0.5%。[2]Skandalakis JE, Gray SW, Ricketts R, et al. The small intestines. In: Skandalakis JE, Gray SW, eds. Embryology for surgeons, 2nd ed. Baltimore, MD: Williams & Wilkins; 1994:184.有临床症状的患者估计为每6000活产婴儿出现1例。[3]Byrne WJ. Disorders of the intestine and pancreas. In: Taeusch WH, Ballard RA, Avery ME, eds. Disease of the newborn. Philadelphia, PA: WB Saunders; 1991:586-693.